RESUMO
An 85-year-old female with situs inversus totalis was admitted due to obstructive jaundice, secondary to multiple choledocholithiasis and distal biliary stenosis due to adenocarcinoma of the head of the pancreas, with duodenal infiltration and metastatic liver disease. An endoscopic retrograde cholangiopancreatography (ERCP) was attempted in the supine position but bile duct cannulation was not possible due to duodenal infiltration. Finally, a palliative biliary stent was placed percutaneously, with resolution of the jaundice.
Assuntos
Coledocolitíase , Icterícia Obstrutiva , Situs Inversus , Idoso de 80 Anos ou mais , Colangiopancreatografia Retrógrada Endoscópica , Coledocolitíase/complicações , Coledocolitíase/diagnóstico por imagem , Coledocolitíase/cirurgia , Duodeno , Feminino , Humanos , Icterícia Obstrutiva/diagnóstico por imagem , Icterícia Obstrutiva/etiologia , Situs Inversus/complicações , Situs Inversus/diagnóstico por imagemRESUMO
La Telangiectasia Hemorrágica Hereditaria o Enfermedad de Rendu-OslerWeber, es una entidad infradiagnosticada y el retraso diagnóstico es frecuente, lo que va a dificultar el screening y tratamiento preventivo de los pacientes y de sus familiares afectos. Presentamos el caso de una paciente que debutó con una complicación grave de la enfermedad, a pesar de lo cual el diagnóstico de la enfermedad no se realizó hasta pasados 10 años. (AU)
Hereditary heamorrhagic telangiectasia or Rendu Osler disease is an underdiagnosed condition with long diagnostic delay time which will make difficult the screening and early treatment of patients and affected family members. We report a case of a patient diagnosed 10 years lapsing from initial onset of severe complications of the disease (AU)
